Anti-beta glucuronidase抗體,β葡萄糖醛酸苷酶抗體科研產品介紹：
Defects in GUSB are the cause of mucopolysaccharidosis type 7 (MPS7) ; also known as Sly syndrome. MPS7 is an autosomal recessive lysosomal storage disease characterized by inability to degrade glucuronic acid-containing glycosaminoglycans. The phenotype is highly variable, ranging from severe lethal hydrops fetalis to mild forms with survival into adulthood. Most patients with the intermediate phenotype show hepatomegaly, skeletal anomalies, coarse facies, and variable degrees of mental impairment. Mucopolysaccharidosis type 7 is associated with non-immune hydrops fetalis, a generalized edema of the fetus with fluid accumulation in the body cavities due to non-immune causes. Non-immune hydrops fetalis is not a diagnosis in itself but a symptom, a feature of many genetic disorders, and the end-stage of a wide variety of disorders.
與“Anti-beta glucuronidase抗體,β葡萄糖醛酸苷酶抗體科研"有關的產品：
Anti-CK7 (Cytokeratin 7)ret mouse 抗細胞角蛋白7抗體(大、小鼠)
Anti-CK5+6 (Cytokeratin 5+6) 細胞角蛋白5+6抗體
Anti-CK6 (Cytokeratin 6) 細胞角蛋白6抗體
Anti-CK8(Cytokeratin 8) 細胞角蛋白8抗體
Anti-CKLFSF2（human）（chemokine-like factor superfamily 2） 人類新細胞因子/趨化素樣因子超家族成員2抗體
Anti-CK1+5+10+14 高分子量角蛋白抗體
Anti-CK-HMW 高分子量細胞角蛋白抗體
anti-CKIP-1（casein kinase 2 interaction protein 1） 酪蛋白激酶2相互作用蛋白1抗體
Anti-Clostridium perfringens type D 兔抗D型產氣莢膜梭菌抗體
Anti-CLCA4(Calcium-activated chloride channel 4) 鈣激活氯離子通道4抗體
產品詳情：
產品編號：HRK-7980R
產品規格: 0.1ml/0.2ml
產品別名：asd; Beta G1; Beta glucuronidase; Beta-G1; Beta-glucuronidase; BG; BGLR; BGLR_HUMAN; Glucuronidase beta; Gur; Gus; Gus-r; Gus-s; Gus-t; Gus-u; GUSB; Gut; MPS7; Ac2-223
產品價格：詢價(電詢或客服)
產品用途：科研實驗
貯 存： 貯存于-20℃.
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