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當(dāng)前位置:華瑞科研網(wǎng)-ELISA試劑盒>>科研抗體>>科研一抗>>Anti-CCDC40抗體,卷曲螺旋結(jié)構(gòu)域蛋白40抗體科研

Anti-CCDC40抗體,卷曲螺旋結(jié)構(gòu)域蛋白40抗體科研

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所  在  地上海市

聯(lián)系方式:韓經(jīng)理查看聯(lián)系方式

更新時間:2018-05-02 23:16:15瀏覽次數(shù):205次

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商鋪產(chǎn)品:9992條

所在地區(qū):上海上海市

聯(lián)系人:韓經(jīng)理 (銷售)

產(chǎn)品簡介

“Anti-CCDC40抗體,卷曲螺旋結(jié)構(gòu)域蛋白40抗體科研“我公司擁有*的細(xì)胞服務(wù)技術(shù),*的儀器設(shè)備和專業(yè)的ELISA檢測試劑盒、生物索標(biāo)記、熒光索標(biāo)記、酶標(biāo)記等,廣泛用于多種分析研究與技術(shù)測定。咨詢,我們將竭誠為你服務(wù)!

詳細(xì)介紹

Anti-CCDC40抗體,卷曲螺旋結(jié)構(gòu)域蛋白40抗體科研產(chǎn)品介紹:

Required for assembly of dynein regulatory complex (DRC) and inner dynein arm complexes, which are responsible for ciliary beat regulation, thereby playing a central role in motility in cilia and flagella. Not required for outer dynein arm complexes assembly. Required for axonemal recruitment of CCDC39.
Involvement in disease:
Defects in CCDC40 are the cause of primary ciliary dyskinesia type 15 (CILD15) . A disorder characterized by abnormalities of motile cilia. Respiratory infections leading to chronic inflammation and bronchiectasis are recurrent, due to defects in the respiratory cilia; reduced fertility is often observed in male patients due to abnormalities of sperm tails. Half of the patients exhibit randomization of left-right body asymmetry and situs inversus, due to dysfunction of monocilia at the embryonic node. Primary ciliary dyskinesia associated with situs inversus is referred to as Kartagener syndrome. 


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產(chǎn)品詳情:
產(chǎn)品編號:HRK-8091R
產(chǎn)品規(guī)格: 0.1ml/0.2ml
產(chǎn)品別名:CCD40_HUMAN; ccdc 40; CCDC40; Coiled coil domain containing 40; coiled-coil domain containing 40; Coiled-coil domain-containing protein 40
產(chǎn)品價格:詢價(電詢或客服)
產(chǎn)品用途:科研實驗
貯 存:   貯存于-20℃.

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